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Commission on Classification and Terminology

Table 3: Electro-clinical syndromes and other epilepsies

 

Electro-clinical syndromes arranged by age at onset *

Neonatal period
        Benign familial neonatal seizures (BFNS)
        Early myoclonic encephalopathy (EME)
        Ohtahara syndrome

Infancy
        Migrating partial seizures of infancy
        West syndrome
        Myoclonic epilepsy in infancy (MEI)
        Benign infantile seizures
        Benign familial infantile seizures
        Dravet syndrome
        Myoclonic encephalopathy in nonprogressive disorders

Childhood
        Febrile seizures plus (FS+) (can start in infancy)
        Early onset benign childhood occipital epilepsy (Panayiotopoulos type)
        Epilepsy with myoclonic atonic (previously astatic) seizures
        Benign epilepsy with centrotemporal spikes (BECTS)
        Autosomal-dominant nocturnal frontal lobe epilepsy (ADNFLE)
        Late onset childhood occipital epilepsy (Gastaut type)
        Epilepsy with myoclonic absences
        Lennox-Gastaut syndrome
        Epileptic encephalopathy with continuous spike-and-wave during sleep (CSWS)
                      including: Landau-Kleffner syndrome (LKS)
        Childhood absence epilepsy (CAE)

Adolescence - Adult
        Juvenile absence epilepsy (JAE)
        Juvenile myoclonic epilepsy (JME)
        Epilepsy with generalized tonic-clonic seizures alone
        Progressive myoclonus epilepsies (PME)
        Autosomal dominant partial epilepsy with auditory features (ADPEAF)
        Other familial temporal lobe epilepsies

Less Specific Age Relationship *
       
Familial focal epilepsy with variable foci (childhood to adult)
        Reflex epilepsies   

Distinctive Constellations
        Mesial temporal lobe epilepsy with hippocampal sclerosis (MTLE with HS)
        Rasmussen syndrome
        Gelastic seizures with hypothalamic hamartoma

Epilepsies that do not fit into any of these diagnostic categories can be distinguished first on the basis of the presence or absence of a known structural or metabolic condition (presumed cause) and then on the basis of the primary mode of seizure onset (generalized versus focal).

Epilepsies attributed to and organized by structural-metabolic causes
Malformations of Cortical development (hemimeganencephaly, hetertopias etc)
Neurocutaneous syndromes (Tuberous sclerosis complex, Sturge-Weber, etc)
Tumor
Infection
Trauma
Angioma
Peri-natal insults
Stroke
Etc.

Epilepsies of unknown cause

Conditions with epileptic seizures that are traditionally not diagnosed as a form of epilepsy per se.
        Benign neonatal seizures (BNS)
        Febrile seizures (FS)

 

*This arrangement does not reflect etiology.